Acute Motor Axonal Neuropathy 1례

A Case of Acute Motor Axonal Neuropathy

저자들은 임상적으로나 뇌척수액 검사 소견상 Guillain-Barré 증후군과 유사하나 전기 생리학적 검사로 축삭 병변 소견을 보여 acute motor axonal neuropahty로 진단된 1례를 문헌고찰과 함께 보고하는 바이다.

In northern China, annual epidemics of acute-onset flaccid paralysis diagnosed clinically Guillain-Barre syndrome have been observed for at least 20 years. These patients had a distinctive pattern that shares clinical and cerebrospinal fluid findings with demyelinating Guillain-Barré syndrome. But it was different from Guillain-Barré syndrome physiologically and pathologically. Electrodiagnostic studies showed normal motor distal latencies and limb conduction velocity, but reduced compound muscle action potential amplitude. When sensory nerve action potentials are elicitable, F waves are within the range of normal. This disorder was named acute motor axonal neuropathy characterized pathologically by motor nerve fiber degeneration of variable severity and by sparing of sensory fibers. Recovery is usually complete. We experienced a case of acute axonal motor neuropathy, and reported the case with a review of literature.