내경동맥 폐색으로 유발된 무뇌수두증 1례

A Case of Hydranencephaly Caused by Internal Carotid Artery Occlusion

저자들은 두위의 지속적인 증가를 주소로 내원한 9개월된 남아에서 시행한 자기공명 혈관 조영술상 양측 내경동맥의 완전 폐색에 의한 무뇌수두증을 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Hydranencephaly is a condition in which cerebral hemisheres are absent and reduced to fluid-filled sacs in a normal skull. Numerous causes have been proposed, but bilateral occlusion of the internal carotid arteries during early fetal development can explain most of the pathologic abnormalities. We evaluated a case of hydranencephaly by brain CT and magnetic resonance angiography. Magnetic resonance angiography showed flow within the vertebral and basilar arteries without internal carotid intracranial flow above the supraclinoid segment. A brief review of the related literature was given on this subject.