Dandy Walker 증후군이 동반된 Neurocutaneous Giant Melanosis 1례

A Case of Neurocutaneous Giant Melanosis Associated with Dandy-Walker Syndrome

저자들은 3세 남아에서 Dandy-Walker 증후군이 동반된 neurocutaneous giant melanosis 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Neurocutaneous melanosis is a rate congenital phacomatosis, characterized by the presence of multiple pigmented skin nevi at birth. Meningeal melanosis tending to become malignant and seizure. Dandy-Walker syndrome is a developmental disorder of brain characterized by cystic dilatation of the fourth ventricle and agenesis of hypoplasia of the cerebellat vermis. We studied a case of Dandy-Walker syndrome with neurocutaneous giant melanosis in a 3 years old boy.

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