소아 피부근염 1례

A Case of Juvenile Dermatomyositis

저자들은 전신 쇠약감, 피부 발진을 주소로 입원한 6세 남아에서 근생검으로 피부근염을 확진하였고 정주용 면역글로불린, 스테로이드, methotrxate 투여 및 물리치료로 임상 증상과 검사 소견이 호전되었다.

Juvenile dermatomyositis is an uncommon autoimmune disease with classic heliotrope discoloration of eyelids, erythematous skin rash of joints and proximal muscle weakness. Quite different from adults, malignancy is rarely accompanied in juvenile dermatomyositis. However vasculitis, muscle atrophy, calcification and gastrointestinal involvement are often observed in juvenile dermatomyositis. A six year old boy was admitted with chief complaints of general weakness and skin rash. Muscle biopsy was performed which was consistent with dermatomyositis. The patient was treated with intravenous immunoglobulin, steroid, methotrexate and physiotherapy. We report a case of juvenile dermatomyositis.