식욕부진과 성장발달지연으로 내원한 소아의 맥락총 유두종 1례

A Case of Choroid Plexus Papilloma of a Child with Anorexia and Failure to Thrive

저자들은 성장 발달 지연과 식욕 부진의 비특이적인 증상을 보인 환아에서 신경학적 검사상 조화운동불능보행과 울 때 눈과 입이 비대칭적으로 편위되어 시행하였던 뇌단층촬영과 뇌자기공명영상에서 제4뇌실에 발생한 맥락총 유두종을 조기에 진단할 수 있었으며, 완전 절제술을 시행하여 안면마비 및 보행 장애 호전을 보인 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Choroid plexus papilloma is a very rare disease in children. The manifestations of the disease differ according to the tumor size and the location. Increased CSF production by the tumor, hydrocephalus and symptoms of increased ICP are the main symptoms. The first line of treatment is surgical excision, but sometimes excision itself is very difficult due to the site and the size of mass. Adjunctive radiation therapy or chemotherapy is not recommended. Since gross total resection without adjunctive therapy offers highest likelihood of success. Significant prognostic factors are sex, age, time of diagnosis, the duration between the appearance of symptoms and diagnosis, tumor volume, tumor site and the extent of surgery. We report a case of choroid plexus papilloma, in a child with anorexia and failure to thrive.