6개월 여아에서 일측성으로 발생한 급성 파종성 뇌척수염 1례

A Case of Acute Disseminated Encephalomyelitis: Unilateral Involvement in A 6 Month-old Female Infant

A six months old female infant was admitted with an abrupt onset of high fever and prolonged left hemiconvulsion followed by left hemiparesis. She hand a history of an acute upper respiratory tract infection with improvement two weeks before the admission. On admssion, EEG showed lazy phenomenon in the right side and diffuse slowing on the right hemisphere. MRI revealed multiple patchy lesions of high signal intensity in the right basal ganglia and periventricular areas on the T2WI. There was no abnormal finding on the magnetic resonance angiography. She had recovered with conservative treatmen and the unilateral brain lesions were progressively disappeared on the follow-up MRI studies. These unilateral demyelination lesions might be considered as one of the causes of acute infantile hemiplegia or hemiconvulsion-hemiplegia syndrome(HHS) in infancy, and the ADEM should be included as a cause of HHS.