68세 여자의 눈물주머니에 생긴 원발성 횡문근육종

Primary Rhabdomyosarcoma of the Lacrimal Sac in a 68-year-old Woman

Purpose: Rhabdomyosarcoma of the lacrimal sac is extremely rare. There has only been one case in this country, during the 30s, and to our knowledge, there are no reports of primary rhabdomyosarcoma on the lacrimal sac. We report a case of primary rhabdomyosarcoma of the lacrimal sac in a 68-year-old woman Methods: A 68-year-old female patient presented with tearing of the right eye. A lacrimal sac mass extending to the proximal nasolacrimal duct was detected during the dacryocystorhinostomy, and incisional biopsy was performed. Histopathology revealed a rhabdomyosarcoma of the right lacrimal sac. After systemic chemotherapy, complete excision of the tumor through the medial maxilla was performed. Results: The pathologic diagnosis of the excised mass was embryonal type rhabdomyosarcoma. There was no evidence of tumor recurrence in the lacrimal sac or paranasal sinus during 9 months of follow-up. Conclusions: Although rhabdomyosarcoma is very uncommon, this case provides the rationale for including it in differential diagnosis of a mass in lacrimal sac.