알포트 증후군과 동반된 양안 장액망막박리 1예

Bilateral Serous Retinal Detachment Associated With Alport’s Syndrome

Purpose: To report a case of bilateral serous retinal detachment associated with Alport’s syndrome that resolved following intensive blood pressure control and electrolyte imbalance correction. Case summary: A 50-year-old male patient presented with bilateral lenticonus and bilateral serous retinal detachment. Bilateral serous retinal detachment with retinal flecks characteristic of Alport’s syndrome appeared along with the development of chronic renal failure and hypertension. The following kidney biopsy revealed Alport’s syndrome. After 14 days, the serous detachment resolved and vision recovered following intensive blood pressure control and electrolyte imbalance correction fundus and FA results were nearly normal. Conclusions: In this case, bilateral serous retinal detachment in Alport’s syndrome resolved with intensive blood pressure control and electrolyte imbalance correction. To the author’s knowledge, this is the first case in South Korea with documentation of the onset and resolution of bilateral serous retinal detachment in Alport’s syndrome. J Korean Ophthalmol Soc 2010;51(3):463-468