국소 아밀로이드증(Amyloidosis)이 동반된 안와 점막연관 림프조직형 림프종(MALT lymphoma) 1예

Primary Orbital MALT Lymphoma Associated with Localized Amyloidosis

Purpose: To report a case of primary orbital MALT lymphoma with localized amyloidosis. Case summary: A 61-year-old male visited our clinic with diplopia, which had developed approximately 5 months earlier. Magnetic resonance imaging of the orbit showed an ill-defined well-enhanced mass in the left inferior orbit. Incisional biopsy of the orbital mass was performed. Histopathological examination revealed diffuse deposits of an amorphous, eosinophilic substance in the extracellular matrix and vessels with lymphocytes infiltration. Lymphocytes were positive for the immunohistochemical stain against the CD20 and κ-light chain antigens. The amorphous material stained positive for κ-light chain antigen, and Congo red staining showed birefringence. Conclusions: We report a rare case of primary orbital MALT lymphoma associated with localized amyloidosis.