하악골에서 두개저까지 광범위하게 발생한 신경섬유종의 치험례

A case report of surgical removal of neurofibroma that occured on mandibular angle area and spread to skull base

Neurofibroma is a benign tumor arising from nerve fiber. It is classified as solitary type and multiple type which is seen in von Recklinghausen s disease. In oral and maxillofacial region, it originates from the 5th and 7th cranial nerves and occurs on tongue, lip, palate and other oral mucosa. Mass occured, it diagnosed on the basis of the X-ray findings, immunohistochemical studies, and cyst, and other odontogenic tumor, etc. Recurrence rate is about 30% but malignant change is rare. Close observation should be required for solitary lesion because it may be a early sign of von Recklinghausen s disease. In present report, the solitary type neurofibroma in left mandibular angle and skull base was removed and mandiblectomy was performed. Mandible reconstruction was done with long titanium plate and artificial condylar head. Patients asymmetric face has improved. Careful attention will be paid to the prognosis of the patient.