안면부의 선천성 침윤성 지방종증

Congenital infiltrating lipomatosis of the face : report of a case

Congenital infiltrating lipomatosis of the face is a very rare congenital facial lesion composed of proliferating and infiltrating adipose tissue. This is a report of a case that deals with congenital infiltrating lipomatosis of the face. A 7-year-old boy visited the Chonnam University Hospital in January, 1988, with chief complaint of diffuse swlling of the left face and lip. A soft tissue tumor with indistinct boundary was noted and was diagnosed as congenital infiltrating lipomatosis by clinical and histologic examination. The patient underwent wide local excision through modified Weber-Ferguson incision. Surgical specimen was composed of fat tissue with yellow and shiny surface and sized about 90×60×20mm. The lesion was congenital in origin. The mass was a nonencapsulated proliferative mature adipose tissue, being infiltrated to adjacent soft tissues, such as muscles and subcutaneous tissue. Fibrous tissue with various nerve bundles and vessels was observed, but lipoblasts or signs of maligancy was not found. And hypertrophy of underlying maxillary bone was noted. NO evidence of recurrence was shown for 4-year follow up.