頭蓋顔面異形成患者의 腸骨移植을 利用한 上顎水平骨切斷術의 治驗例

A CASE REPORT OF LE FORT Ⅰ OSTEOTOMY WITH ILIAC BONE GRAFT IN CLEIDOCRANIAL DYSOSTOSIS

Genetics and corrective surgery are not only partners in providing for classification, diagnosis, and comprehensive patient care but also in understanding the etiology of the craniofacial anomalies. Cleidocranial dysostosis having a dominant Mendelian inheritance is a rare disease of unknown etiology. The auther have met 21-year-old male with malar and maxillary hypoplasia, prolonged retention of the multiple deciduous teeth, 31 impacted teeth, absence of clavicle, widened sagittal suture and fontaneles. Surgical removal of impacted teeth was done via splitting external cortical bone to preserve remaining bone. After 6 months, the entire maxilla are advanced and moved to inferior with iliac bone graft, and the ramus oblique osteotomy are done on mandible. We have achieved good esthetic and good functional results.