Crouzon 증후군 환아에서 시신경 감압

Optic Canal Decompression in a Child with Crouzon’s Syndrome

Six-year old boy with Crouzon’s syndrome underwent reconstruction and frontoorbital advancement for brachycephaly 3 years ago. The vision of the left eye had been gradually decreased for 3 months recently. Finger count apart from 30cm was failed. Visual acuity of the right eye was 0.4. The optic disc of the left eye was pale. Visual evoked potentials (VEP) of the left side showed the delayed latency compared with that of the right side. There was no symptom of increased intracranial pressure. Extradural anterior clinoidectomy and optic canal decompression was performed via small temporal craniotomy. The vision of the left eye was improved to 0.05. We report a case of Crouzon’s syndrome underwent optic canal decompression for the treatment of visual deterioration. Optic canal decompression could be effective for vision recovery in patients with Crouzon’s syndrome initially underwent craniofacial surgery.