뇌하수체선종으로 오인된 터키안 내 연골양 척삭종

Intrasellar chondroid chordoma mimicking pituitary adenoma

Chordomas are rare, slow-growing malignant tumors of the midline, representing approximately 0.1 to 0.2% of intracranial neoplasms. We describe the case of intrasellar chondroid chordoma, hardly distinguished from pituitary adenoma. Initially, the lesion was considered to be a nonfunctioning pituitary adenoma. After endoscopic endonasal approach, the tumor was subtotally removed, and the histopathological diagnosis was a chondroid chordoma. The patient underwent Gamma Knife radiosurgery. Although this tumor is easily misdiagnosed, initial aggressive surgical resection and gamma knife radiosurgery can yield a favorable prognosis.