선천성 악골유합증

Syngnathia; Review of literature and a case report

Congenital craniofacial disorders represent approxin1ately 20% of all birth defects. One of these disorders is syngnathia. Congenital fusion of the maxilla and mandible is rare and can present in a wide range of severity from single mucosa! band(synechiae) to complete bony fusion(syngnathia). Syngnathia, congenital bony fusion of the mandible and maxilla, is even less common than synechiae, with only 25 cases reported in the literature. Most of them have presented as an incomplete, unilateral fusion. We report a case of unilateral bony fusion of the maxilla, mandible, and zygomatic arch. Details of operative management and follow-up data are presented witl1 review of literature.